Impaired Very Long-chain Acyl-CoA β-Oxidation in Human X-linked Adrenoleukodystrophy Fibroblasts Is a Direct Consequence of ABCD1 Transporter Dysfunction

Intrinsic acyl-CoA thioesterase activity of a peroxisomal ATP binding cassette transporter is required for transport and metabolism of fatty acids

(2013) Carine De Marcos Lousa et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

ABC Transporters and Immunity: Mechanism of Self-Defense

(2012) Andreas Hinz et al.   BIOCHEMISTRY

Peroxisomal acyl-CoA synthetases

(2012) Paul A. Watkins et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Peroxisomal ABC transporters: Structure, function and role in disease

(2012) Masashi Morita et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

X-linked adrenoleukodystrophy: Clinical, metabolic, genetic and pathophysiological aspects

(2012) Stephan Kemp et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Peroxisomal Fatty Acid Uptake Mechanism inSaccharomyces cerevisiae

(2012) Carlo W. T. van Roermund et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mutations in ABCD4 cause a new inborn error of vitamin B12 metabolism

(2012) David Coelho et al.   NATURE GENETICS

The human geneSLC25A17encodes a peroxisomal transporter of coenzyme A, FAD and NAD+

(2011) Gennaro Agrimi et al.   BIOCHEMICAL JOURNAL

Transfer of metabolites across the peroxisomal membrane

(2011) Vasily D. Antonenkov et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Structural Requirements for Interaction of Peroxisomal Targeting Signal 2 and Its Receptor PEX7

(2011) Markus Kunze et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Differential substrate specificities of human ABCD1 and ABCD2 in peroxisomal fatty acid β-oxidation

(2010) Carlo W.T. van Roermund et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS

General Aspects and Neuropathology of X-Linked Adrenoleukodystrophy

(2010) Isidro Ferrer et al.   BRAIN PATHOLOGY

Current and Future Pharmacological Treatment Strategies in X-Linked Adrenoleukodystrophy

(2010) Johannes Berger et al.   BRAIN PATHOLOGY

The role of ELOVL1 in very long-chain fatty acid homeostasis and X-linked adrenoleukodystrophy

(2010) Rob Ofman et al.   EMBO Molecular Medicine

70-kDa peroxisomal membrane protein related protein (P70R/ABCD4) localizes to endoplasmic reticulum not peroxisomes, and NH2-terminal hydrophobic property determines the subcellular localization of ABC subfamily D proteins

(2008) Yoshinori Kashiwayama et al.   EXPERIMENTAL CELL RESEARCH

The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters

(2008) Carlo W. T. van Roermund et al.   FASEB JOURNAL