Loss of the thyroid hormone-binding protein Crym renders striatal neurons more vulnerable to mutant huntingtin in Huntington's disease

Impaired Brain Energy Metabolism in the BACHD Mouse Model of Huntington's Disease: Critical Role of Astrocyte–Neuron Interactions

(2014) Lydie Boussicault et al.   JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM

Thyroid hormone receptors and resistance to thyroid hormone disorders

(2014) Tânia M. Ortiga-Carvalho et al.   Nature Reviews Endocrinology

A restricted population of CB1 cannabinoid receptors with neuroprotective activity

(2014) A. Chiarlone et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Possible involvement of self-defense mechanisms in the preferential vulnerability of the striatum in Huntington's disease

(2014) Laetitia Francelle et al.   Frontiers in Cellular Neuroscience

A role of mitochondrial complex II defects in genetic models of Huntington's disease expressing N-terminal fragments of mutant huntingtin

(2013) Maria Damiano et al.   HUMAN MOLECULAR GENETICS

Releasing the brake: restoring fast axonal transport in neurodegenerative disorders

(2013) Maria-Victoria Hinckelmann et al.   TRENDS IN CELL BIOLOGY

Capucin does not modify the toxicity of a mutant Huntingtin fragment in vivo

(2012) Laurie Galvan et al.   NEUROBIOLOGY OF AGING

Resequencing of 29 Candidate Genes in Patients With Familial and Sporadic Amyotrophic Lateral Sclerosis

(2011) Hussein Daoud et al.   ARCHIVES OF NEUROLOGY

Mitogen- and stress-activated protein kinase 1-induced neuroprotection in Huntington's disease: role on chromatin remodeling at the PGC-1-alpha promoter

(2011) Elodie Martin et al.   HUMAN MOLECULAR GENETICS

Mammalian forebrain ketimine reductase identified as μ-crystallin; potential regulation by thyroid hormones

(2011) André Hallen et al.   JOURNAL OF NEUROCHEMISTRY

Worsening of Huntington disease phenotype in CB1 receptor knockout mice

(2011) Stéphane Mievis et al.   NEUROBIOLOGY OF DISEASE

Viral-mediated overexpression of mutant huntingtin to model HD in various species

(2011) Marta Ruiz et al.   NEUROBIOLOGY OF DISEASE

What have we learned from gene expression profiles in Huntington's disease?

(2011) Tamara Seredenina et al.   NEUROBIOLOGY OF DISEASE

Decreased Striatal RGS2 Expression Is Neuroprotective in Huntington's Disease (HD) and Exemplifies a Compensatory Aspect of HD-Induced Gene Regulation

(2011) Tamara Seredenina et al.   PLoS One

In vivo expression of polyglutamine-expanded huntingtin by mouse striatal astrocytes impairs glutamate transport: a correlation with Huntington's disease subjects

(2010) M. Faideau et al.   HUMAN MOLECULAR GENETICS

Sustained effects of nonallele-specificHuntingtinsilencing

(2009) Valérie Drouet et al.   ANNALS OF NEUROLOGY

Mitochondria in Huntington's disease

(2009) Maria Damiano et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Pathophysiology of Huntingtonʼs disease: from huntingtin functions to potential treatments

(2009) Emmanuel Roze et al.   CURRENT OPINION IN NEUROLOGY

Neuroendocrine Disturbances in Huntington's Disease

(2009) Nadine Saleh et al.   PLoS One

Normal Aging Modulates the Neurotoxicity of Mutant Huntingtin

(2009) Elsa Diguet et al.   PLoS One

Rhes, a Striatal Specific Protein, Mediates Mutant-Huntingtin Cytotoxicity

(2009) S. Subramaniam et al.   SCIENCE

Implication of the JNK pathway in a rat model of Huntington's disease

(2008) V. Perrin et al.   EXPERIMENTAL NEUROLOGY

Dopamine determines the vulnerability of striatal neurons to the N-terminal fragment of mutant huntingtin through the regulation of mitochondrial complex II

(2008) Alexandra Benchoua et al.   HUMAN MOLECULAR GENETICS

Full-Length Human Mutant Huntingtin with a Stable Polyglutamine Repeat Can Elicit Progressive and Selective Neuropathogenesis in BACHD Mice

(2008) M. Gray et al.   JOURNAL OF NEUROSCIENCE

Functional roles for the striatal-enriched transcription factor, Bcl11b, in the control of striatal gene expression and transcriptional dysregulation in Huntington's disease

(2008) Paula A. Desplats et al.   NEUROBIOLOGY OF DISEASE

Quantitative gene expression profiling of mouse brain regions reveals differential transcripts conserved in human and affected in disease models

(2008) Camille Brochier et al.   PHYSIOLOGICAL GENOMICS

Mitogen- and stress-activated protein kinase-1 deficiency is involved in expanded-huntingtin-induced transcriptional dysregulation and striatal death

(2007) Emmanuel Roze et al.   FASEB JOURNAL

Haloperidol protects striatal neurons from dysfunction induced by mutated huntingtin in vivo

(2007) Delphine Charvin et al.   NEUROBIOLOGY OF DISEASE