Substitutions at residue 211 in the prion protein drive a switch between CJD and GSS syndrome, a new mechanism governing inherited neurodegenerative disorders

Prion protein gene M232R variation is probably an uncommon polymorphism rather than a pathogenic mutation

(2011) Jon Beck et al.   BRAIN

The oligomerization properties of prion protein are restricted to the H2H3 domain

(2010) Nesrine Chakroun et al.   FASEB JOURNAL

Estimating prion concentration in fluids and tissues by quantitative PMCA

(2010) Baian Chen et al.   NATURE METHODS

Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt–Jakob disease: its effect on the phenotype and prion-type characteristics

(2009) Ignazio Cali et al.   BRAIN

Glimepiride Reduces the Expression of PrPC, Prevents PrPSc Formation and Protects against Prion Mediated Neurotoxicity

(2009) Clive Bate et al.   PLoS One

The Prion's Elusive Reason for Being

(2008) Adriano Aguzzi et al.   Annual Review of Neuroscience

Crossing the Species Barrier by PrPSc Replication In Vitro Generates Unique Infectious Prions

(2008) Joaquín Castilla et al.   CELL

Cell-free propagation of prion strains

(2008) Joaquín Castilla et al.   EMBO JOURNAL

Scrapie Prion Protein Structural Constraints Obtained by Limited Proteolysis and Mass Spectrometry

(2008) Gustavo Sajnani et al.   JOURNAL OF MOLECULAR BIOLOGY

Effects of human PrPSc type and PRNP genotype in an in-vitro conversion assay

(2008) Michael Jones et al.   NEUROREPORT

Prominent and Persistent Extraneural Infection in Human PrP Transgenic Mice Infected with Variant CJD

(2008) Vincent Béringue et al.   PLoS One

Regulating Factors of PrPres Glycosylation in Creutzfeldt-Jakob Disease - Implications for the Dissemination and the Diagnosis of Human Prion Strains

(2008) Etienne Levavasseur et al.   PLoS One